Thanks to advancements in care, Cystic Fibrosis patients are leading longer, healthier and more productive lives.
Cystic Fibrosis, commonly referred to as CF, is a genetic disease that, in part, places patients at risk of lung infections. Mucus builds up in the lungs and other organs, restrict the airways and other pathways, creating complications including lung damage over time. This damage can cause respiratory failure and impact several natural processes in the body.
Because CF is a progressive disease, it’s important to identify the disease in the early stages and seek treatment to assist the body’s functions. CF is usually identified by key symptoms such as shortness of breath, coughing and wheezing, an inability to maintain proper weight and difficulty with bowel movements.
Care for CF patients can include a variety of treatment options. Total Care RX works closely with referring physicians charged with patient care to ensure strict adherence to each patient's specific program.
These are inhaled medications that thin mucus in the airways.
Modulator therapies are designed to correct the malfunctioning protein made by the CFTR gene.
Because CF patients are more susceptible to infection from bacteria, antibiotics can be an effective option to eradicate bacteria and sustain a patient’s health.
A nebulizer generates mist from liquid medications that allow the patient to inhale the solution through the use of a nebulizer. It’s important to pair specific medication with the nebulizer recommended by the manufacturer. When using a nebulizer at home it’s imperative to follow the proper cleaning instructions to ensure a sterile environment. Nebulizers should always be cleaned, disinfected, thoroughly rinsed and air dried.
Ultimately some CF patients may be candidates for a lung transplant.
— Courtesy of Cystic Fibrosis Foundation
Patients start their treatments with inhaled Bronchodilators such as Albuterol inhalers, which opens up the airways and increases air flow to the lungs.
Hypertonic saline is used to mobilize mucus so it’s easier to cough out.
Pulmozyme may be prescribed to thin and loosen the mucus to make it easier for patients to clear their lungs.
Patients undergo chest physiotherapy, donning an inflatable vest attached to a machine that performs high-frequency vibrations to loosen the mucus.
Inhaled antibiotics may be taken again. Some patients will use oral azithromycin or a similar antibiotic from once a day to three times a week to reduce inflammation of the airways.
Some CF patients will eventually need to have a lung transplant. Total Care RX will be there every step of the way, from pre- to post-operation, to ensure patients receive the best treatments possible.
Total Care RX believes strongly that support groups help bring people together and provide a common ground for those suffering from similar medical conditions. The sharing of experiences, feelings and coping strategies can become a major part of the healing process.
Total Care RX is proud to be a Live2Thrive partner as this program offers tremendous support, free vitamins/supplements, copay assistance and much more.
Total Care RX is also proud to be partners with two renown Cystic Fibrosis organizations in the Cystic Fibrosis Foundation and the Boomer Esiason Foundation. Both of these staples of the Cystic Fibrosis community have always provided tireless support for all people with CF.